Tuberous sclerosis and fibrous dysplasia.

نویسندگان

  • Emerson L Gasparetto
  • Arnolfo de Carvalho Neto
  • Isac Bruck
  • Sergio Antoniuk
چکیده

We present the case of an 11-year-old female patient with tuberous sclerosis who had a right nasal mass. CT examination revealed fibrous dysplasia involving the frontal, ethmoid, sphenoid, and vomer bones. Biopsy findings of the mass confirmed this diagnosis, and follow-up revealed marked expansion of these lesions. The authors emphasize the association of bone abnormalities and tuberous sclerosis and discuss the consideration of fibrous dysplasia as a component of this syndrome.

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عنوان ژورنال:
  • AJNR. American journal of neuroradiology

دوره 24 5  شماره 

صفحات  -

تاریخ انتشار 2003